This is a case of giant congenital melanocytic nevus, associated with a single lipoma & multiple satellite lesions. Biopsy report showed skin with groups of nevoid cells extending into underlying fat, intimately associated with the lobules & surrounding many blood vessels. The systemic examination was normal. This is a typical case of a giant congenital melanocytic nevus with satellite lesions and a lipoma association. As the surface area is greater than 40cm in diameter; the risk of developing melanoma is higher.