Abstract

Plexiform Neurofibroma of the Occipital Scalp with Occipital Bone Defect and Neurofibromatosis Type 1- A Case Report in a Tertiary Care Center, AP, India

Plexiform neurofibromas are virtually pathognomonic of NF-1. They are generally bulky tumours usually associated with major nerve trunks and plexuses. They are rope-like, diffusely, infiltrating, non-circumscribed lesions that resemble a bag of warms. The scalp and orbits are common sites. Most PNFs remain benign and only 10%-15% of deep-seated PNFs are at risk of developing into MPNSTs. Here we report a case of PNF of the occipital scalp in a 12-year-old male child with an occipital bone defect associated with NF-1.

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